Skeletal cystic angiomatosis with severe hip joint deformation resembling massive osteolysis

An aggressive destruction pattern resulting in joint deformation has not be en described in skeletal cystic angiomatosis (SCA) so far. We present the c ase of a 6-year-old boy with such findings strongly resembling Gorham's dis ease (massive osteolysis). Since the prognosis of the latter entity tends t o be less favorable than in SCA, particularly SCA without extraskeletal inv olvement, careful differentiation of both disorders appears to be important .