Prenatal sonographic diagnosis of Klippel-Trenaunay-Weber syndrome with cardiac failure

This report describes the prenatal sonographic diagnosis of a case of Klipp el-Trenaunay-Weber syndrome. The sonographic appearance of this disorder wa s characterized by the presence of multiple distorted cystic areas involvin g the right leg and abdomen and cardiomegaly with early fetal heart failure . Despite the prenatal detection of the extensive cutaneous and visceral in volvement, the infant died soon after birth of high-output cardiac failure and Ka-sabach-Merritt syndrome. (C) 2001 John Wiley & Sons, Inc.