We report a patient with Gardner's syndrome who, in addition to a total col
ectomy, had multiple excisions of desmoid tumors in both thighs. He present
ed with left-sided neck swelling and pain. MRI was highly suggestive of des
moid tumors in multiple neck muscles. To our knowledge this is the first de
scription of diffuse fibromatosis of the neck in association with Gardner's
syndrome.