Eosinophilic pustular folliculitis in association with nevoid basal cell carcinoma syndrome

This study reports on the clinical and Light microscopic features of a nevo id basal cell carcinoma syndrome with the complication of eosinophilic pust ular folliculitis. To the authors' knowledge, this is the first report of s uch an association, which is possibly due to immune dysregulation. Moreover , the patient experienced remission of eosinophilic pustular folliculitis a fter removal of the jaw cyst. One possible explanation for the remission is that a long-lasting TH, type inflammatory response as a result of the bone defect produces effective cytokines such as interferon-gamma.