An infant with a cardiac murmur was found to have a patent arterial duct an
d an anomalous left pulmonary artery. The duct was surgically ligated at th
e age of 8 months, and she remained free of cardiac or respiratory symptoms
up to her death at 6 years from an unrelated intestinal condition. An anom
aly was discovered at post mortem examination; the left pulmonary artery ar
ose from the right pulmonary artery and passed behind the trachea to enter
the left lung. We describe and illustrate the anatomic features of this wel
l-recognized entity, discuss the embryological substrate, and refer to the
clinical implications. (C) 2001 Wiley-Liss, Inc.