Surgical treatment of a tomaculous neuropathy

Compressive neuropathy of the ulnar nerve at the elbow is the second most c ommon nerve entrapment in the upper limb. Eight possible anatomical points of constriction have been identified. The most common constriction being th e intermuscular septum proximally or between the two heads of the flexor ca rpi ulnaris in the cubital canal distally. Surgical release is successful i n 80-90% of cases. Certain rare genetic conditions can predispose susceptib le peripheral nerves to similar compressive neuropathies but there is no li terature on surgical treatment of such patients. We present a case of hered itary neuropathy with liability to pressure palsy (HNPP) often known as 'to maculous' neuropathy, in a patient with ulnar nerve symptoms who underwent a surgical release.