Pleuropulmonary blastoma

We report a rare case of pleuropulmonary blastoma arising in a 3-year-old b oy and involving the middle and upper lobes of the right lung. Radical rese ction of the mass was achieved by a bilobectomy. Microscopic examination of the histologic sections showed the typical findings of blastemal and mesen chymal areas with focal zones of rhabdomyoblastic and liposarcomatous diffe rentiation. Monthly cycles of chemotherapy consisting of ifosfamide, vincri stine and actinomycin D were given for 10 months after surgical resection. Our patient is presently alive and disease-free two years after diagnosis. As complete tumour ablation is essential to prevent local recurrence and al low any chance of survival, the favourable outcome of our patient is probab ly due to the radical resection of the neoplasm.