Angiodysplasia with osteohypertrophy affecting the oromaxillofacial area: Clinical findings

The authors report a case of oro-facial port-wine stain angiomatosis with c utaneous and mucosal lesions localized in the first and the second branch s urface distribution areas of the right trigeminal nerve in association with right upper and lower lip, cheek, and hemimaxillary true hypertrophy leadi ng to a severe dento-skeletal malocclusion with open-bite and facial asymme try. The authors through a revision of the Bibliography locate nosologicall y this case among the rare congenital angiodysplastic syndromes affecting t he maxillo-facial district as the Sturge-Weber and the Klippel-Trenaunay sy ndromes. They debate also about etiopathogenetic, clinical, differential di agnosis, and therapeutic aspects concerning the treatment of patients affec ted by this kind of malformation.