Glomangiosarcoma, or malignant glomus tumor, is a very rare neoplasm that w
hen seen typically arises from a benign glomus tumor. Despite having histol
ogic features of malignancy, these tumors usually do not metastasize. Howev
er, when metastasis occurs this disease is often fatal. We report a case of
a malignant glomus tumor arising de novo on the nose of an 89-year-old whi
te woman, and we review the literature concerning glomangiosarcomas.