Anaesthetic management of an adolescent for scoliosis surgery with a Fontan circulation

Advances in the treatment of congenital heart disease have led to a new gro up of adolescents or adults patients with cardiac anomalies. The anaestheti c management of these patients can be challenging especially when they are scheduled for major noncardiac surgery inducing haemodynamic instability. W e report the case of a 14-year-old boy scheduled for posterior spinal fusio n for idiopathic scoliosis who underwent a Fontan operation in infancy for pulmonary atresia with right ventricle hypoplasia. The preoperative investi gations and the anaesthetic management are described.