The Chiari III malformation: an unusual and asymptomatic variant in an 11-year old child

Chiari III malformation is an extremely rare condition, and is characterize d by the hindbrain herniation into a low occipital or high cervical encepha locele together with the pathologic and imaging features of the Chiari II m alformation. In this report, an unusual variant of the Chiari III malformat ion was diagnosed in an 11-year-old girl. She had an encephalocele operatio n when she was a newborn, and has been asymptomatic since then. The clinica l and imaging findings of this case were presented. (C) 2001 Elsevier Scien ce Ireland Ltd. All rights reserved.