Background. A retrospective review was carried out of nine children un
der 17 years of age with a diagnosis of intramedullary tumor seen duri
ng the period 1989-1995. Six had astrocytomas; one each had an ependym
oma, a PNET, and a choroid plexus papilloma. Five patients had back pa
in, 3 others had mild pareses and the ninth had incapacitating defects
. Seven of the 9 were treated by subtotal extirpation of the lesion, a
nd biopsy alone was performed in the other two. All tumors were low gr
ade (grade I or II) and therefore radiation therapy (RT) was performed
as the only postoperative treatment in 8 of the 9 children. Results.
In February 1996, seven (77.8%) children were alive and two (22.2%) di
ed of recurrent tumor (7 months and 5 years after diagnosis, respectiv
ely). Median follow-up was 3 years 4 months (range: 1 year 6 months to
7 years 3 months). Conclusion. Surgical removal of intraspinal tumors
provides the best hope of control, but spinal column deformity after
laminectomy and irradiation is a serious long-term problem in children
. Orthopedic supervision for the prevention of these deformities; e.g.
, by external immobilization, is mandatory. (C) 1997 Wiley-Liss, Inc.