Keratosis pilaris and hereditary koilonychia without monilethrix

Keratosis pilaris is found commonly in isolation as well as associated with other conditions. We describe a family with keratosis pilaris and heredita ry koilonychia, with an autosomal dominant pattern of inheritance. These tw o findings have only been previously found in the context of monilethrix. T he coexistence of the two disorders suggests a close association of their g enetic pathogenesis.