Hereditary benign intraepithelial dyskeratosis: Report of two cases with prominent oral lesions

Hereditary benign intraepithelial dyskeratosis is a rare autosomal dominant disorder of the oral and ocular mucosa initially described in the Haliwa-S aponi Native American tribe of North Carolina. We describe 2 sisters with t he characteristic oral and ocular findings. This entity should be distingui shed from several other diseases that cause white lesions in the mouth incl uding white sponge nevus.