Focal eosinophilic myositis

Idiopathic hypereosinophilic syndrome (HES) is a heterogeneous group of dis orders with the common features of prolonged eosinophilia of underdetermine d cause and multiple organ system dysfunction. Focal eosinophilic myositis is an uncommon manifestation of HES. We report a case of focal eosinophilic myositis with tender muscle swelling followed by proximal weakness, but wi thout non-systemic symptoms and muscle trophism in the lower limbs. Muscle biopsy specimen showed acute myositis with eosinophil infiltration. Electro myographic features were typical of myositis. The clinical and biochemical response to corticosteroids was excellent, and a relapse that occurred beca use the steroid dose was not lowered, responded well.