Solitary fibrous tumor of the orbit in a child

Citation
Lm. Lucci et al., Solitary fibrous tumor of the orbit in a child, OPHTHAL PL, 17(5), 2001, pp. 369-373
Citations number
16
Categorie Soggetti
Optalmology
Journal title
OPHTHALMIC PLASTIC AND RECONSTRUCTIVE SURGERY
ISSN journal
07409303 → ACNP
Volume
17
Issue
5
Year of publication
2001
Pages
369 - 373
Database
ISI
SICI code
0740-9303(200109)17:5<369:SFTOTO>2.0.ZU;2-P
Abstract
Purpose: Solitary fibrous tumor is a rare spindle-cell tumor that usually i s seen in the pleura. The orbit is one of the most common extrapleural site s. It is frequently misdiagnosed as hemangiopericytoma and is seen in older patients. We present the youngest case of this tumor, which was apparent i n family photographs by age 10 and removed at age 15. The first reported ec hography findings are presented. Methods: Case report and literature review. Results. Solitary fibrous tumor was diagnosed by microscopy and immunohisto chemical study that showed cells reactive with vimentin and CD34. Conclusions: Solitary fibrous tumor of the orbit has been diagnosed with in creasing frequency in recent years as the result of improved methods of pat hologic examination. It is important to be aware of this tumor and recogniz e that it must be included in the differential diagnosis of highly vascular spindle-cell tumors even in young children.