Oculocutaneous albinism is a rare autosomal recessive disorder characterize
d by general depigmentation. nystagmus, photophobia, and decreased visual a
cuity. Malignant melanoma is extremely rare in patients with albinism. We p
resent a 41-year-old albino mate patient. who was admitted with a suspected
bronchogenic carcinoma. He underwent a pulmonary resection and the diagnos
is was primary malign melanoma of the lung. The patient died of tumor recur
rence in the postoperative 46th month. (C) 2001 Elsevier Science B.V. All r
ights reserved.