Here we report 3 cases of renal oncocytoma with a dominating small cell com
ponent arising in adult women. These 3 cases of small cell variant of renal
oncocytoma were found among 134 cases of oncocytomas of the kidney in the
routine and consultation files of the authors. Two of 3 cases were initiall
y thought to be a malignant tumor by the referring pathologists. In all 3 c
ases minor areas of the tumors, which were identical to the classical renal
oncocytomas were found. The small cell areas were arranged in a characteri
stic organoid pattern different front all the known types of the renal beni
gn and malignant tumors. We summarize all morphologic, immunohistochemical,
and Ultrastructural features of this unusual oncocytoma variant with regar
d to its differential diagnosis.