Objective-To examine the prevalence of congenital heart disease in babies w
ith oesophageal atresia and its influence on outcome.
Design-Retrospective analysis.
Setting-The resident population of one health region.
Results-A total of 153 babies with oesophageal atresia were identified from
509 975 live births (0.30 per 1000); 26 (17%) had cardiac defects. Surviva
l of babies with normal hearts was 97%, 97%, and 95% at one week, one month
, and one year. Survival of babies with congenital heart disease was 85%, 8
5%, and 67% at one week, one month, and one year, but only one of ten death
s was the result of the congenital heart disease. The remaining deaths were
due to other congenital malformations, respiratory disease, or chromosome
abnormalities.
Conclusions-There is a high prevalence of congenital heart disease in babie
s with oesophageal atresia. Congenital heart disease is associated with a h
igher mortality in oesophageal atresia but it is not the cause of it.