The hereditary motor-sensory neuropathy Charcot-Marie-Tooth disease: a case report and a review of the literature

A 53-year-old woman diagnosed as having hereditary motor-sensory neuropathy Charcot-Marie-Tooth (CMT) disease Type 2, underwent inguinal hernia surger y. In this patient CMT disease was manifested as distal muscle weakness and wasting. Ana esthetic experience with patients who have CMT disease is lim ited. Association to malignant hyperthermia is very unlikely although there is one case report that shows that there could be a relationship. We descr ibe a total intravenous anaesthesia (TIVA) protocol with propofol and alfen tanil without any muscle relaxants after fiberoptic intubation. The patient made an uneventful recovery and was discharged from the hospital on the fo urth postoperative day. TIVA was a safe technique in this patient and shoul d be considered as an alternative for patients presenting with CMT disease.