Extraneural metastasis in a child with atypical teratoid rhabdoid tumor ofthe central nervous system

Atypical teratoid rhabdoid tumor is a distinctive brain tumor appearing in infancy and early childhood. Leptomeningeal dissemination is common, both a t presentation and relapse. Extracranial metastases of the central nervous system tumors are rarely seen. To our knowledge there is only one report wi th an atypical teratoid rhabdoid tumor metastasizing via a ventriculoperito neal shunt. We describe the first case of atypical teratoid rhabdoid tumor of the central nervous system who developed lung metastasis without the pre sence of a shunt.