Congenital factor X deficiency is a rare inherited coagulation disorder, ch
aracterized by prolonged prothrombin time and partial thromboplastin time.
For the definite diagnosis, specific factor X level should be investigated.
We describe a patient with factor X deficiency who had intracranial hemorr
hage. Hematologic tests showed prolonged prothrombin time, partial thrombop
lastin time, and a factor X level of 5%. The patient's hemorrhage resolved
with fresh frozen plasma replacement. In this article, we discuss the clini
cal features and management of factor X deficiency.