U. Boggi et al., SURVIVING CATASTROPHIC GASTROINTESTINAL INVOLVEMENT DUE TO CHURG-STRAUSS-SYNDROME - REPORT OF A CASE, Hepato-gastroenterology, 44(16), 1997, pp. 1169-1171
Gastrointestinal (GI) involvement is not rarely encountered in Churg-S
trauss syndrome (CSS), We describe the case of a young white woman pre
senting with acute acalculous cholecystitis, who subsequently develope
d despite prompt administration of immunosuppressive therapy, Life thr
eatening GI involvement, requiring multiple operations, Over a 7-month
period the patient eventually recovered from her disease. Forty-two m
onths Later she is free from symptoms, with Low daily doses (6 mg) of
oral methylprednisolone. Although medical and surgical complications o
f CSS may develop while the patient is undergoing therapy, early diagn
osis with joint surgical and medical management is essential to bring
the disease under control.