At the age of 4 years, a total cavopulmonary connection was performed in a
boy with a complex congenital heart defect. On addition, a DDDR pacemaker w
as implanted for sick sinus syndrome. Atrial and ventricular leads were epi
cardially placed at the left atrium and left ventricle. At the age of 10 ye
ars, a new epicardial ventricular lead was placed because of malfunction of
the existing lead. At the some operation the pulse generator was replaced
by a Medtronic Kappa DR 731. After replacement, the boy experienced episode
s of phrenic nerve stimulation associated with feelings of discomfort. Holt
er recordings revealed ventricular stimulation from the atrial stimulus for
2 consecutive beats. This phenomenon repeated exactly every 3 hours and wa
s caused by the automatic lead impedance measurement that used a 5-V, 1-ms
stimulus output.