Purpose. - To define the epidemiology and clinical features of Behcet's dis
ease, giving special attention to unusual forms.
Methods. - We retrospectively reviewed the medical records of 309 cases wit
h joint manifestations among 450 cases of Behcet's disease seen over a 20-y
ear period who met the International Study Group of Behcet's disease criter
ia.
Results. - Joint manifestations were present in 68.3% and were inaugural in
34.5%. The knee and ankles were the joints most commonly affected. Monoart
hritis, oligoarthritis and polyarthritis were seen respectively in 12, 13.5
and 19.8%. Sacroiliitis is observed in 6%. Unusual forms included destruct
ive polyarthritis (two cases), popliteal cyst (two cases), myositis (two ca
ses) and ankylosing spondylitis (two cases).
Conclusion. - Joint manifestations are common in Behcet's disease. They are
frequently associated with erythema nodosum and necrotic pseudofolliculiti
s. Polyarthritis is not rare. Their unusual forms deserve to be known. (C)
2001 Editions scientifiques et medicales Elsevier SAS.