MALIGNANT EPITHELIAL SKIN TUMORS IN HERED ITARY HEMORRHAGIC TELANGIECTASIA (OSLER-WEBER-RENDU-SYNDROME)

Citation
H. Breuninger et al., MALIGNANT EPITHELIAL SKIN TUMORS IN HERED ITARY HEMORRHAGIC TELANGIECTASIA (OSLER-WEBER-RENDU-SYNDROME), Hautarzt, 48(7), 1997, pp. 496-499
Citations number
8
Categorie Soggetti
Dermatology & Venereal Diseases
Journal title
ISSN journal
00178470
Volume
48
Issue
7
Year of publication
1997
Pages
496 - 499
Database
ISI
SICI code
0017-8470(1997)48:7<496:MESTIH>2.0.ZU;2-V
Abstract
A 65 year old male patient was diagnosed with hereditary hemorrhagic t elangiectasia at 30. During recent years he has suffered frequent, alm ost daily, nose bleeds causing anemia and making several blood transfu sions necessary. In the past 2-3 years,the patient has developed multi ple squamous cell carcinomas on the face. These un-unsually large tumo urs were treated by micrographic surgery using paraffin sections and t he defects closed with a variety of flaps and grafts. Several solar ke ratoses were also removed. If hemostasis parameters are normal, skin s urgery can be performed without hestitation in hereditary hemorrhagic telangiectasia.