Imaging of pulmonary manifestations in subtype B of Niemann-Pick disease

Authors
Duchateau, F Dechambre, S Coche, E
Citation
F. Duchateau et al., Imaging of pulmonary manifestations in subtype B of Niemann-Pick disease, BR J RADIOL, 74(887), 2001, pp. 1059-1061
Citations number
5
Categorie Soggetti
Radiology ,Nuclear Medicine & Imaging","Medical Research Diagnosis & Treatment
Journal title
BRITISH JOURNAL OF RADIOLOGY
ISSN journal
00071285 → ACNP
Volume
74
Issue
887
Year of publication
2001
Pages
1059 - 1061
Database
ISI
SICI code
Abstract
We report the radiological and high resolution CT (HRCT) findings of the pu lmonary involvement in a case of subtype B Niemann-Pick disease. diagnosed in an asymptomatic 22-year-old man, which was proved by bone marrow biopsy and sphingomyelinase assessment. In the present case, HRCT showed smooth in terlobular septa thickening and a subtle ground-glass pattern.