J. Watson et al., An exception to the rule: Ectopic ACTH production from functional neuroendocrine tissue in an ovarian dermoid cyst, J ENDOC INV, 24(10), 2001, pp. 802-805
Ectopic ACTH production accounts for 15% of Cushing's syndrome presentation
s and is characterized by the presence of an excess of ACTH precursors. How
ever in the case presented here ectopic ACTH production was from functional
pituitary tissue within an ovarian dermoid cyst. Endocrine investigations
showed that the problem behaved more like pituitary-dependent Cushing's dis
ease and this is discussed. Furthermore, this case is one of familial dermo
id cysts, another unusual phenomenon. (C) 2001, Editrice Kurtis.