Advances in congenital heart surgery have resulted in. the increased surviv
al of infants born with complex congenital heart disease. Questions remain,
however, about how these patients will develop and whether they will have
normal, productive lives. To date,,studies have shown that although the vas
t majority of children with congenital heart disease have normal outcomes,
as a group they generally have higher rates of neurodevelopmental problems.
The developmental sequelae include mild problems in cognition, attention,
and neuromotor functioning. The etiology of neurologic deficits in this pop
ulation appears to be multifactorial with preoperative, operative, and post
operative factors all contributing to outcome. Continued research and attem
pts to minimize neurologic injury and associated sequelae are. of primary i
mportance. Recent data suggest that advances in care already may be improvi
ng, outcome after congenital heart surgery. Ongoing documentation of the lo
ng-term outcome in this population needs to be mandated, as does the implem
entation of environmental enrichment programs to help ameliorate the long-t
erm consequences of congenital heart disease. Curr Opin. Pediatr 2001, 13:4
82-486 (C) 2001 Lippincott Williams & Wilkins, Inc.