Adenoid cystic carcinoma of the vulva: Conservative surgery using a de-epithelized rhomboid flap

Adenoid cystic carcinoma of the vulva is a very rare entity manifested by a n indolent clinical course, late recurrence and a propensity for perineural and local invasion. A 41-year-old women underwent radical local excision and ipsilateral superf icial lymph-node dissection using a de-epithelized rhomboid flap for adenoi d cystic carcinoma of the left vulva. On follow-up after two years the pati ent is alive and well with no evidence of disease. In this report we present the first case of adenoid cystic carcinoma of the vulva using a de-epithelized rhomboid flap.