Leiomyoma at the site of esophageal atresia repair

Esophageal leiomyomas are rare in the pediatric population. They frequently occur in association with other anomalies, such as Alport's syndrome, oste oarthropathy, and leiomyomas elsewhere in the body. The authors describe th e case of a focal esophageal leiomyoma in a 12-month-old girl with a histor y of long-gap esophageal atresia. The patient initially underwent bouginage of the proximal pouch while awaiting definitive repair. After esophageal r epair, the patient required multiple dilatations for anastomotic strictures . A segmental resection of the esophagus was performed because of recurrent strictures. A leiomyoma, arising from the site of the previous esophageal atresia repair, was noted on histologic evaluation. Esophageal leiomyomas h ave not been reported previously in a child with esophageal atresia. Copyri ght (C) 2001 by W.B. Saunders Company.