Acinic cell carcinoma of the lacrimal gland with intracranial extension - A case report

Purpose: To describe a patient with acinic cell carcinoma of the lacrimal g land presenting with atypical manifestations including erosion of the orbit al roof and intracranial extension. We compare his clinical manifestations with two previously reported cases. Methods: Case report. Results. A 51-year-old man presented with a firm, tender, palpable mass in the superior temporal portion of his right orbit. CT scan demonstrated a la rge homogeneously enhancing mass displacing the globe inferiorly and erodin g the roof of the orbit. MRI of the orbit showed intracranial extension of tumor. Biopsy revealed an acinic cell carcinoma of the lacrimal gland. Conclusions: Acinic cell carcinoma is a rare neoplasm occurring primarily i n the major and minor salivary glands.