We are reporting on tile case of a 46XY male patient that presented a bilat
eral testicular seminoma in the setting of bilateral cryptorchidia and left
inguinal hernia. The patient received flue courses of cisplatin/ciclophosp
hamide followed by 3 000 cGy of radiation. The patient then, underwent rese
ction of the residual mass and of art unrecognizable pelvic structure. The
histopathalogical analysis revealed necrosis of tile residual seminoma and
an atrophic uterus. Currently, the patient is alive and asymptomatic at 88
months of follow-up. This is tire third case reported of a patient with per
sistent mullerian duct syndrome and bilateral seminoma.