A ventilator-dependent patient with primary ciliary dyskinesia underwent su
ccessful living-donor lobar lung transplantation. The case was a 24-year-ol
d woman who had developed recurrent lower respiratory infection and became
ventilator-dependent due to severe bronchiectasis. Transmission electron mi
croscopy of the resected bronchus demonstrated inner dynein arm deficiency.
(C) 2001 by The Society of Thoracic Surgeons.