A 63-year-old man had a distal arch aneurysm combined with a circumflex ret
roesophageal right aortic arch, which is a rare form of vascular ring. By u
sing combined median sternotomy and left thoracotomy under deep hypothermia
and retrograde cerebral perfusion, total arch replacement with a vascular
graft was successful. We describe our surgical strategy for arch aneurysm a
ssociated with an uncommon congenital vascular malformation. (C) 2001 by Th
e Society of Thoracic Surgeons.