The authors describe a patient with histologically confirmed pulmonary lymp
hangiomyomatosis and thin-section computed tomography findings mimicking La
ngerhans cell histioctytosis. The description emphasizes the nonspecificity
of the computed tomography findings in this patient. This report also sugg
ests that the computed tomography diagnosis of lymphangioleiomyomatosis can
be difficult at an early stage of the disease and should be complemented b
y biopsy verification.