OBJECTIVE AND IMPORTANCE: An arachnoid cyst at the craniocervical junction
presenting with obstructive hydrocephalus as a result of blockage of the ou
tflow of the fourth ventricle is described. This is a very rare anatomic si
te, with only five other cases described in the literature.
CLINICAL PRESENTATION: A 37-year-old woman presented with a 9-month history
of severe neck pain, persistent vomiting, visual disturbances, and numbnes
s of the nose, cheek, and lips. She had severe bilateral papilledema on oph
thalmoscopy. Magnetic resonance imaging revealed a midline cystic lesion ex
tending down to C2.
INTERVENTION: The patient underwent posterior fossa craniectomy and excisio
n of the arachnoid cyst. She made a full recovery and was asymptomatic at f
ollow-up examination.
CONCLUSION: The symptomatology of these rare craniocervical arachnoid cysts
and their development are discussed.