Primary pulmonary rhabdomyosarcoma arising within cystic adenomatoid malformation: A case report and review of the literature

The current report describes a 13-month-old boy with primary pulmonary rhab domyosarcoma (RMS) that originated within a congenital cystic adenomatoid m alformation (CCAM). To the best of our knowledge, he is the youngest patien t of all primary pulmonary RMS cases reported in the English-language liter ature. The tumor, localized in left upper lobe, was removed completely, and histologic examination showed embryonal subtype. Postoperative systemic ch emotherapy was carried out. Recent evaluation 15 months after resection has not identified any residual or recurrent disease. Primary pulmonary RMS, a lthough very rare in the pediatric age group, should be considered in young patients with solitary pulmonary masses and associated cystic lesions. Cop yright (C) 2001 by W.B. Saunders Company.