Primary pulmonary rhabdomyosarcoma: Report of a case in an adult and review of the literature

A case of primary pulmonary rhabdomyosarcoma occurring in a 62-year-old man is reported, and a review of the literature is presented. The tumor affect ed the left upper lobe and involved the mediastinal lymph nodes. Immunohist ochemical and ultrastructural studies supported the myogenic phenotype of t he neoplasm. A left pneumonectomy was performed with complete surgical remo val of the tumor. Postoperative radiotherapy was carried out. The patient i s currently alive and free of disease 9 months after operation. Despite the rarity of primary pulmonary rhabdomyosarcoma, this tumor should be differe ntiated from other poorly differentiated pulmonary neoplasms and from metas tatic sarcomas.