Idiopathic congenital bilateral vocal cord paralysis (BVCP) can occur as an
isolated abnormality or as part of a multisystem disorder. The chromosomal
abnormalities found in 4 children who presented with idiopathic congenital
BVCP in association with other congenital abnormalities between January 19
91 and April 1999 are described. Three children had abductor paralysis, and
tracheostomy was required in I. The fourth child had adductor paralysis an
d required a feeding gastrostomy for management of aspiration. There was no
clinically significant improvement in vocal cord function observed in any
child. Idiopathic congenital BVCP. when associated with other congenital di
sorders, may occur as a consequence of an underlying chromosomal abnormalit
y, and chromosome studies should be performed in this group of children. Si
milarly, the possibility of vocal cord dysfunction should be considered in
children who are found to have chromosomal abnormalities. A chromosomal abn
ormality appears to preclude the possibility of early spontaneous improveme
nt in vocal cord function.