Pleuropulmonary blastoma in congenital cystic adenomatoid malformation: Report of a case

Pulmonary blastoma is a rare malignant tumor seen in both adults and childr en. Approximately only 25% of cases occur in pediatric patients, many of wh am affected by a congenital pulmonary cystic lesion. The clinical features, radiological findings and management of a 3-year-old boy affected by a pul monary blastoma which arose in a congenital cystic adenomatoid malformation are reported, and an extensive review of the literature is also made. Beca use of the well-known tendency of cystic pulmonary diseases to develop mali gnancies, authors recommend the surgical excision of these kind of lesion o r at least their close radiological follow-up.