Intramedullary metastases from a non neurogenic cancer are relatively rare,
representing approximately 1-2,1% of metastatic sites according to publish
ed autopsy reports. Their association with syrinx is extremely rare. Four c
ases have been described in the last 30 years. We report the case of a 60 y
ear old female with past medical historiy of Peutz-Jeghers disease, who pre
sented with clinical signs suggestive of medullary lesions of the cervical
spine. MR imaging showed tumoral lesions at different levels associed with
syrinx. Surgical biopsy confirmed the intramedullary lesions which, by path
ology, were found to be of metastatic origin.