Objective: This article reviews teratomas, neoplasms composed of the t
hree germinal layers of the embryo that form tissues foreign to the pa
rt in which they arise. These are most common in the sacrococcygeal re
gion and are rare in the head and neck. In this region, major concerns
are airway obstruction and cosmesis. Method: Pathology records at two
tertiary care paediatric hospitals were reviewed for diagnoses of hea
d and neck teratomas. This revealed nine cases between 1983 and 1993,
five males and four females. Two males were stillborn. Five were cervi
cal, two were in the nasopharynx, and two were facial. The lesions wer
e immature in two cases and mature in the remainder. All of the livebo
rn children underwent surgery within the first year of life, and only
one required tracheotomy. Results: One child had recurrence of teratom
atous tissue diagnosed with CT, which was treated surgically. The chil
d has remained free of tumour for over 3 years. Pathogenesis, clinical
appearance, diagnostic work-up, and currently accepted modes of thera
py are reviewed.