Extraovarian granulosa cell tumor

A 54-year-old woman was admitted to our hospital complaining of postcoital bleeding. Sonography of the abdomen showed a 8.2 x 8.9cm-sized solid hetero geneous mass occupying the cul-de-sac, which appeared to be in no way conne cted with the ovary. On exploratory laparotomy, the tumor mass protruded fr om the posterolateral retroperitoneum of the pelvic cavity and severely rep laced the uterus and adnexa with the outer surface being grossly intact. It grossly measured 10 cm in maximal diameter. The histologic features closel y resembled those of ovarian granulosa cell tumor. The primary extraovarian granulosa cell tumor is extremely rare such that in the English literature only 7 cases have been reported to date. Of those granulosa cell tumors ar e especially rare and only two cases have been reported to arise from retro peritoneum. We herein present a case of retroperitoneal granulosa cell tumo r with special regard to differential diagnosis from other solid tumors wit h similar histology.