HYDROCEPHALUS AND CHRONICALLY INCREASED INTRACRANIAL-PRESSURE IN ACHONDROPLASIA

Two achondroplastic children with ventriculomegaly are reported. The p atients had no signs of increased intracranial pressure, but in one bl indness had previously been detected by the parents. Neuroradiological examinations showed ventriculomegaly in both. Intracranial pressure r emained at high levels (20-55 mmHg) preoperatively; ventriculo-periton eal shunting was performed in both cases, and postoperatively levels f ell to normal (5-16 mmHg). The need for the treatment of ventriculomeg aly seen in achondroplastic children is analyzed on the basis of these two patients, with a brief review of literature.