A case of malignant schwannoma occurring in an 11-year-old boy is desc
ribed. To our knowledge, this is the third case of malignant juxta-adr
enal schwannoma reported in the literature. It was misdiagnosed at the
onset of the disease as a post-traumatic renal hematoma. Angiography
revealed that the tumor derived its blood supply from collateral vesse
ls of the aorta, splenic, and left gastric arteries. An analysis of th
e diagnosis, clinical course, and prognostic factors of this rare tumo
r is performed.