PERIANAL FETAL RHABDOMYOMA - CASE-REPORT

A 4-week-old female was referred with a firm, enlarging perianal mass present since birth. At surgery, the lesion appeared to be arising fro m the subcutaneous external sphincter, Local excision was successful w ith preservation of the external sphincter. Histologic examination sho wed a mixture of undifferentiated spindle cells as well as immature an d maturing myofibers consistent with a fetal rhabdomyoma, This report represents the second case of a fetal rhabdomyoma arising in the peria nal location. All pediatric cases of fetal rhabdomyoma in the literatu re are reviewed.