Background. Pulmonary valve incompetence is usually well tolerated aft
er tetralogy of Fallot repair but may result in late progressive right
heart failure as manifested by increasing fatigue, dyspnea, and frequ
ently arrhythmias. Methods. All patients who underwent pulmonary valve
replacement in our center late after repair of tetralogy of Fallot we
re reviewed. Results. Eighty-five patients had elective pulmonary valv
e replacement late (median, 9.3 years) after repair. Operative risk wa
s low (1.1%). Ninety percent of survivors are in New York Heart Associ
ation class I. Survival 10 years after pulmonary valve replacement is
95%, with 86% of the patients free of reoperation for valve failure. C
onclusions. Pulmonary valve replacement is infrequently required after
repair of tetralogy of Fallot. Pulmonary valve replacement may be per
formed electively with little risk; it improves symptoms of right hear
t failure and provides satisfactory long-term survival with low risk o
f early valve failure. As the population of patients who have had repa
ir of tetralogy of Fallot ages, pulmonary valve replacement will becom
e a more frequent consideration. (C) 1997 by The Society of Thoracic S
urgeons.