An infant with truncus arteriosus and severe dysfunction of the trunca
l valve including both stenosis and insufficiency successfully underwe
nt primary repair. This included the insertion of two separate valved
homograft conduits. Early outcome has been excellent and the patient i
s doing well after 6 months with only echocardiographic evidence of mi
ld aortic valve regurgitation. Double-homograft repair is a realistic
option in cases of truncus arteriosus with severe malformation of the
truncal valve.