We report the case of a 56-year-old male with a sebaceous nevus of the
scalp, complicated by multiple tumor development. Histologic examinat
ion revealed a basal cell carcinoma, a syringocystadenoma papilliferum
and a proliferating trichilemmal cyst. Sebaceous nevus has a well-doc
umented neoplastic potential. Multiple tumors may occasionally arise,
but the coexistence of 3 or more tumors is extremely rare. Close monit
oring and early complete surgical excision of sebaceous nevi are warra
nted, in order to ensure a favorable prognosis.